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VOLUME 2 , ISSUE 2 ( July-December, 2012 ) > List of Articles


Prosthodontic Rehabilitation of Papillon-Lefevre Syndrome

Ilang kumaran R, Srinivasan J, Baburajan K, Anna Ravi Cherian

Keywords : Papillon-Lefevre syndrome, Preventive Prosthodontics, Pa/mar-plantar hyperkeratosis

Citation Information : kumaran R I, J S, K B, Cherian AR. Prosthodontic Rehabilitation of Papillon-Lefevre Syndrome. 2012; 2 (2):61-65.

DOI: 10.5005/jsd-2-2-61

License: CC BY-NC 4.0

Published Online: 30-07-2020

Copyright Statement:  Copyright © 2012; The Author(s).


Papillon-Lefevre syndrome (PLS) is an autosomal recessive genetic disorder. It has a reported incidence of 1-4 persons per million. This syndrome presents with dermatological and dental manifestations. It is usually diagnosed by the presence of palmar-plantar hyperkeratosis of the skin and premature exfoliation of the teeth. This case report describes preventive prosthetic treatment given to 17 year old female patient with PLS who had reported with old unaesthetic denture.

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