Journal of Scientific Dentistry

Register      Login

VOLUME 2 , ISSUE 2 ( July-December, 2012 ) > List of Articles

CASE REPORT

Prosthodontic Rehabilitation of Papillon-Lefevre Syndrome

Ilang kumaran R, Srinivasan J, Baburajan K, Anna Ravi Cherian

Keywords : Pa/mar-plantar hyperkeratosis, Preventive Prosthodontics,Papillon-Lefevre syndrome

Citation Information : kumaran R I, J S, K B, Cherian AR. Prosthodontic Rehabilitation of Papillon-Lefevre Syndrome. 2012; 2 (2):61-65.

DOI: 10.5005/jsd-2-2-61

License: CC BY-NC 4.0

Published Online: 00-12-2012

Copyright Statement:  Copyright © 2012; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Papillon-Lefevre syndrome (PLS) is an autosomal recessive genetic disorder. It has a reported incidence of 1-4 persons per million. This syndrome presents with dermatological and dental manifestations. It is usually diagnosed by the presence of palmar-plantar hyperkeratosis of the skin and premature exfoliation of the teeth. This case report describes preventive prosthetic treatment given to 17 year old female patient with PLS who had reported with old unaesthetic denture.


PDF Share
  1. Rajendran and Sivapathasundaram. editors. Shafer's textbook of oral pathology. 5th ed. Elsevier (India), 2006; pp 560-61.
  2. Patel S, Davidson LE. Papillon-Lefèvre syndrome: A report of two cases. 2004;14:288-94. Int J Paediatric Dent
  3. Kosem R, Debeljak M, Repič Lampret B, Kansky A, Battelino T, Trebušak Podkrajšek K. Cathepsin C gene 5'-Untranslated Region Mutation in Papillon Lefèvre syndrome. Dermatology 2012 [Epub ahead of print].
  4. Keskin-Yıldmm Z, Şimşek-Derelioğlu S, Kantarcı M, Y1lmaz Y, Büyükavcı M. Papillon-Lefèvre syndrome: report of three cases in the same family. Turk J Pediatr 2012;54:171-76.
  5. Rathod VJ, Joshi NV. Papillon-Lefevre syndrome: A report of two cases. Jlndian Soc Periodontol 201 0; 14 (4):275-78.
  6. Page RC, Baab DA. A new look at the etiology and pathogenesis of early onset periodontitis. Cementopathia revisisted. J Periodontal 1985;56(12):748-51.
  7. DeVan MM. The nature of the partial denture foundation: suggestions for its preservation. J Prosthet Dent 1952;2(2):210-18.
  8. Hart TC, Hart PS, Michalec MD, Callison SA, Walker SJ. Mutations of the cathepsin C gene are responsible for Papillon-Lefevre syndrome. J Med Genet 1999;36:881-87.
  9. Taşı PN, Tapşın S, Demirel S, Yaivç ME, Akyuz S, Yarat A, Sabin F. Isolation and Characterization of Dental Pulp Stem cells from a Patient with Papillon-Lefèvre syndrome. J Endod 2013;39:31-8.
  10. Sreeramulu B, Haragopal S, Shalini K, Madhuri D, Sudha, Kiran G. The Prosthodontic Management of a young Edentulous Patient with the Papillon-Lefèvre syndrome -A rare case report. J Clin Diagn Res 2012;6(10):1808-11.
  11. Rűdiger S, Petersilka G, Flemmig TF. Combined systemic and local antimicrobial therapy of periodontal disease in Papillon -Lefevre syndrome. A report of 4 cases. J Clin Periodontol 1999;26:847-54.
  12. Shah P, Shirol D, Lodaya R, Bhat C, Gugwad SC. Rehabilitation of a 3 year old child with Papillon Lefèvre syndrome using telescopic Dentures -A case report. International Contemporary Journal of Dentitry 2010; 1 (1):68-72.
  13. Vikhe DM, Lagdive SB, Gangadhar SA, Bhandari A. Prosthodontic Rehabilitation of Patients with Papillon-Lefevre Syndrome. A case report. Pravara Med Rev 2011;3(4):19-22.
  14. Ahmadian L, Monzavi A, Arbabi R, Hashemi HM. Full-mouth rehabilitation of an edentulous patient with Papillon-Lefèvre syndrome using dental implants: A clinical report. J Prosthodont 2011; 20(8):643-48.
  15. Etoz OA, Ulu M, Kesim B. Treatment of Patient with Papillon-Lefèvre syndrome with short implants: A case report. Implant Dent 2010;19(5):394-99. Authors: 1
PDF Share

© Jaypee Brothers Medical Publishers (P) LTD.