Lip pits are among the rarest congenital deformities recorded. Initially reported in 1845, its familial occurrence has been repofted just once. These developmental anomalies occur either as an isolated defect or in association with other developmental deformities including cleft lip, cleft palate or both. It may be located at the commissures of the lips or in the midline of the lower lip. It is often inherited as an autosomal dominant trait with variable penetrance. We report a case ofcongenital lip pit manifesting in the lower lip in a 12 year old male child.
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